CLINICAL CASE OF A RARE DISEASE IN PEDIATRICS - SYSTEMIC VASCULITIS: WEGENER'S GRANULOMATOSIS (ACR, 1990)
Keywords:
Wegener's granulomatosis, antineutrophilic cytoplasmic antibodies (ANCA).Abstract
Introduction. The Granulomatosis with polyangiitis (GPA) (formerly called Wegener's granulomatosis) is a disease characterized by necrotizing granulomatous inflammation of small and medium-sized blood vessels with a primary disorder that causes injury of the upper respiratory tract, lungs and kidneys. The clinical manifestations of Wegener's granulomatosis are varied.
Clinical case report. This article presents the medical history of a 14-year-old patient diagnosed with Wegener's granulomatosis (Granulomatosis with polyangiitis (GPA)) with analyzes of the clinical manifestations of the disease, diagnostic criteria, and treatment strategy.
Discussion. The presented clinical case demonstrates the diversity of the onset of the disease, which made difficult early diagnostics and selection the treatment strategy.
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