ЖҮЙЕЛІ СКЛЕРОДЕРМИЯМЕН БІРЛЕСКЕН ӨКПЕ ГИПЕРТЕНЗИЯНЫҢ ДИАГНОСТИКАЛЫҚ МӘСЕЛЕЛЕРІ
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https://doi.org/10.31082/1728-452X-2020-215-216-5-6-15-23##semicolon##
жүйелі склеродермия##common.commaListSeparator## өкпе гипертензиясы##common.commaListSeparator## скриниг##common.commaListSeparator## DETECT алгоритмі##common.commaListSeparator## жүректің оң жақ камераларының катетеризациясы##article.abstract##
Жүйелік склеродермия - өкпе гипертензиясымен байланыскан аутоиммунды аурулардың жиі кездесетін түрі болып табылады. Өкпе гипертензиясы ерте өлімнің ықтимал болжаушысы болып табылады, осыған байланысты соңғы уақытта зерттеушілер арасында жүйелік склеродермиямен байланысқан өкпе гипертензияның зерттеу мәселелерінің анықталуына қызығушылық артып келеді.
Мақсаты. Күнделікті клиникалық тәжірибеде қолданылатын жүйелік склеродермиямен байланысты өкпе гипертензиясын тексеру мақсатымен диагностикалық алгоритмдерді қолдану қағидаларын, заманауи диагностикалық мәселелері қарастырыру.
Материал және әдістері. Әдеби деректерді зерттеу мақсатында Web of Science, PubMed/MEDLINE-да 10 жылға дейінгі тереңдікте осы мәселеге қатысты ақпаратты іздеу жүзеге асырылды. Іздеу барысында келесі терминдер жеке және бірге қолданылды: "жүйелі склеродермия", "өкпе гипертензиясы", "DETECT алгоритмі", "жүректің оң камераларын катетеризациялау". Іздеудің негізгі шарты жүйелік склеродермиямен байланысқан өкпе гипертензиясы бар науқастарды зерттеуге негізделген зерттеу жұмыстары болды: мета-анализдер, түпнұсқа зерттеулер, ретроспективті және когорттық зерттеулер.
Нәтижелері және талқылауы. Өкпе гипертензияның клиникалық белгілерінің спецификалық емес болуы, бұл аурудың ерте анықталуын едәуір қиындатады. Өкпе гипертензияның клиникалық көріністері айқын кезеңнің дамуына дейін нақты болмауы диагнозды кеш қойылуына әкеледі. Дәрігердің күнделікті тәжірибесінде қолданылатын негізгі алгоритмдер өкпе гипертензияның диагноз қойылмаған жағдайлар санын азайтуға мүмкіндік береді.
Қорытынды. Жүйелі склеродермиямен байланысқан өкпе гипертензиясының диагностикасы күнделікті дәрігер тәжірибесінде қиындық туғызады. Өкпе гипертензияны ерте анықтау, сонымен қатар уақытылы емдеу өте маңызды, өйткені аталған факторлар жүйелі склеродермиямен ауыратын науқастардың өмір сүру деңгейін жақсартады.
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